Adrenogenital ciwo - duk fasali na pathology

Don siffofin jima'i na farko da na sakandare, halayen suna da alhaki, wasu daga cikinsu ana samarwa a cikin gland. Akwai ƙwayar da ke ciki wadda ke nuna rashin jin dadi daga waɗannan endocrine gland and excessive release of androgens. Rashin haɗarin jima'i a cikin jiki yana haifar da canje-canje mai mahimmanci a tsarin jiki.

Adrenogenital Syndrome - Dalili

Abubuwan da ake tunani a hankali sun fito ne daga maye gurbin kwayoyin halitta wanda ya gaji. Babu wuya a bincikar da shi, yanayin rashin ciwo na adrenogenital shine ƙari guda ɗaya da 5000-6500. Canje-canje a cikin tsarin kwayoyin halitta yana haifar da karuwa a girman da lalacewa na gwanon da ke ciki. Ana rage yawan samar da ƙananan enzymes wanda ke shiga cikin samar da cortisol da aldosterone. Rashin su yana haifar da karuwa a cikin jigilar mazaunan jima'i.

Adrenogenital ciwo - rarrabawa

Dangane da ƙimar adrenocortical da kuma tsananin bayyanar cututtuka, cutar da aka bayyana ta wanzu a yawancin bambancin. Hanyoyin adrenogenital ciwo:

• gishiri-rasa;
• ƙwayar cuta (mai sauki);
• post-pubertal (nonclassical, atypical).

Adrenogenital ciwo - gishiri tsari

Mafi yawan nau'ikan ilimin lissafi, wanda aka gano a jarirai ko yara na farkon shekara ta rayuwa. Tare da ciwon gishiri na adrenogenital, halayen hormonal yana damuwa da kuma aikin gwanon da ke ciki ba shi da kyau. Irin wannan cutar yana tare da ƙananan maida hankali na aldosterone. Dole ne a kula da ma'aunin gishiri a jiki. Wannan ciwo na adrenogenital yana haifar da wani cin zarafin zuciya da kuma tsalle a cikin karfin jini. Wannan yana faruwa a bango na tattara salts a kodan.

Adrenogenital ciwo ne siffar ƙwayar cuta

Kwayar da ke da sauƙi ko na al'ada na tsarin ilimin cututtuka ba tare da abubuwan da suka faru ba. Maganin adrenogenital da aka kwatanta (siffar mai siffar ACS) tana kaiwa kawai ga canje-canje a cikin jikin mutum na waje. Irin wannan cututtuka kuma an gano shi a lokacin da ya fara haihuwa ko nan da nan bayan haihuwa. A cikin tsarin haihuwa ya kasance al'ada.

Postpubertate nau'i na adrenogenital ciwo

Irin wannan cututtukan kuma ana kiranta da ƙananan abubuwa, waɗanda aka samo su da kuma wadanda basu dace ba. Irin wannan ciwo na adrenogenital yana faruwa ne kawai a cikin matan da ke da jima'i. Dalili na ci gaba da ilimin cututtuka na iya zama duka maye gurbin kwayoyin halitta, da kuma ciwon kututtuka . Wannan cututtuka yana sau da yawa tare da rashin haihuwa, saboda haka ba tare da isasshen farilla ba, ciwon adrenogenital da ciki yana da matsala maras kyau. Ko da tare da kyakkyawan haɓaka, hadarin rashin haushi ya yi girma, an kashe tayin a farkon farkon makonni 7-10.

Adrenogenital ciwo - bayyanar cututtuka

Hoto na asibiti wanda aka kwatanta anomaly kwayoyin ya dace da shekaru da kuma irin wannan cuta. Adrenogenital ciwo a cikin jarirai na iya wani lokaci ba za a ƙaddara, saboda abin da jima'i na jariri iya gano kuskure. Alamar alamun bayyanar cututtuka ta zama bayyane daga shekaru 2-4, a wasu lokuta yana nunawa daga baya, a lokacin yaro ko balaga.

Adrenogenital ciwo a cikin yara

Tare da irin gishiri na gishiri, ana lura da alamun yanayin rikici na ruwa-gishiri:

• zawo;
• mummunan zubar da ciki;
• low jini;
• shakatawa;
• tachycardia;
• asarar nauyi.

Ƙananan ciwo na adrenogenital a cikin yara maza yana da wadannan bayyanar cututtuka:

• kara azzakari;
• matsanancin fata pigmentation na scrotum;
• duhu epidermis a kusa da anus.

Yaran yara ba su da alamun bincikar su saboda hoton asibiti a lokacin da aka fara ba shi da kyau. Daga baya (daga 2 shekaru) adrenogenital ciwo ya fi sananne:

• girma daga gashi a jiki, ciki har da al'amuran;
• ƙananan, gruff murya;
• hormonal kuraje ( kuraje vulgaris);
• masculinisation;
• hanzarta ƙaddamarwar kashi;
• gajeren lokaci.

Adrenogenital ciwo a cikin 'yan mata

Don ayyana rashin lafiya a cikin jariran mata ya fi sauƙi, an samu irin wadannan alamun:

• jigon hanzari, wanda yayi kama da azzakari;
• babban labia, kama da lakabi;
• an hada da farji da urethra a cikin sinus urogenital.

Bisa ga ƙarshen alamun jariri, 'yan mata sukan yi kuskure ga wasu yara maza kuma suna haɓaka bisa ga rashin jima'i. Saboda wannan, a makaranta ko yaro, waɗannan yara suna da matsalolin halayyar mutum. A cikin tsarin haifuwa da yarinyar ta dace daidai da jinsin mata, wannan shine dalilin da ya sa ta ji kanta mace. Yaro ya fara rikici da matsala tare da daidaitawa a cikin al'umma.

Bayan shekaru 2, yanayin ciwo na adrenogenital yana da alaƙa da wadannan bayyanar cututtuka:

• rashin cigaba da girma da gashi mai launin gashi;
• gajeren kafafu da makamai;
• muscularity;
• bayyanar gashin ido (ta hanyar shekaru 8);
• jiki mutum (m kafadu, ƙananan kwasfa);
• babu girma na mammary gland;
• low girma da kuma m torso;
• Muryar murya;
• cutar cututtuka;
• marigayi na farko na haila (ba a baya fiye da shekaru 15-16);
• m sake zagayowar, jinkirin jinkiri a haila;
• Aminorrhea ko oligomenorrhea;
• rashin haihuwa;
• Ƙin jini ya girgiza;
• matsanancin pigmentation na epidermis.

Adrenogenital ciwo - ganewar asali

Kayan aiki da bincike-bincike na taimakawa wajen gano hyperplasia da dysfunction na adreal cortex. Don tantance cututtuka na adrenogenital ciwo a cikin jarirai, jarrabawa sosai game da al'amuran da aka lissafta kwaikwayo (ko duban dan tayi). Binciken gwadawa zai iya gano ovaries da mahaifa a cikin 'yan mata da gabobin namiji.

Don tabbatar da tantancewar da ake zargin, an gudanar dakin gwaje-gwaje don maganin ciwon adrenogenital. Ya haɗa da nazarin fitsari da jini akan abun ciki na hormones:

• 17-OH-progesterone;
• aldosterone;
• cortisol;
• 17-ketosteroids.

Bugu da ƙari sanya:

• biochemistry ;
• gwaji na jini;
• bincikar jarrabawar fitsari.

Jiyya na adrenogenital ciwo

Ba zai yiwu ba a kawar da tsarin ilimin kwayoyin halitta, amma ana iya kawar da bayyanannun gwaji. Adrenogenital ciwo - shawarwari na asibiti:

1. Yau daɗin liyafar kwayoyin hormonal. Don daidaita al'amuran ƙwayar cuta da kuma kula da ma'auni na endocrine, za ku buƙaci ku sha glucocorticoids kullum. Abinda ya fi so shine Dexamethasone. Ana lissafi lissafi a kai-tsaye kuma jeri daga 0.05 zuwa 0.25 MG kowace rana. Da nau'in cutar gishiri, yana da muhimmanci a dauki magungunan ma'adinai domin kula da ma'aunin gishiri.
2. Daidaitawar bayyanar. Ana ba da shawara ga marasa lafiya da ƙwararruwar da aka kwatanta da su don samun filastik halayen jiki, gyaran ciki da sauran tsoma baki don tabbatar da cewa al'amuran suna da siffar daidai da girman.
3. Tattaunawa na yau da kullum tare da likitan ɗan adam (akan buƙatar). Wasu marasa lafiya suna buƙatar taimako a daidaitawar zamantakewa da kuma yarda da kansu a matsayin mutum mai cikakken gudu.
4. Tsarkewa daga kwayoyin halitta. Mata da suke so su yi juna biyu suna buƙatar yin amfani da magunguna na musamman da suka tabbatar da gyaran matakan da ake ciki da kuma kawar da samar da inrogene. Ana daukar nauyin glucocorticoids a cikin lokacin gestation.