Gilbert ta ciwo - bayyanar cututtuka

Cinwan ciwon Gilbert (cutar Gilbert, dangin javasice ba tare da hemolytic ba, dangin dangi na dangi, magungunan hyperbilirubinemia na kundin tsarin mulki) wani cututtuka ne tare da wani tafarki marar kyau, wanda ya haifar da maye gurbin kwayar da ke da alhakin bilirubin dake cikin hanta. An ambaci wannan cuta ne bayan da masanin kimiyyar gastroenterologist Faransa Augustine Nicolas Gilbert, wanda ya fara bayyana shi a 1901. Cutar Gilbert tana nuna kanta a matsayin wani nau'in bilirubin mai girma a cikin jini, jaundice da wasu alamomin da ba su da haɗari kuma basu buƙatar magani na gaggawa.

Kwayar cutar ta Gilbert ta ciwo

Babban bayyanar cututtuka na wannan cuta sun haɗa da wadannan:

  1. Jaundice, lokacin da ya fara lura da maganin idanu na ido (daga kusan ba a gane shi ba). A wasu lokuta, akwai yiwuwar ganowa a fata a cikin tarnai na nasolabial, dabino, da tsalle.
  2. Raunin rashin lafiyar a cikin haɗarin hypochondrium na dama, a wasu lokuta, ƙila a sami ƙaramin ƙãra a cikin hanta.
  3. Babban rauni da gajiya.
  4. A wasu lokuta, tashin hankali, haɓakawa, rashin kwakwalwa, rashin haƙuri ga wasu abinci na iya faruwa.

Dalilin matsalar ciwon Gilbert shine rashi a cikin hanta na enzyme na musamman (glucuronyltransferase), wanda ke da alhakin musayar bilirubin. A sakamakon haka, kawai zuwa kashi 30 cikin dari na adadin bile pigment din yana tsinkaye cikin jiki, kuma yawancin ya karu a cikin jini, yana haifar da mafi yawan alamu na wannan cuta - jaundice.

Sanin ganewar cutar ta Gilbert

Sakamakon ganewar cutar ta Gilbert na yawanci ne akan gwajin jini:

  1. Jimlar bilirubin a Gilbert ta ciwo daga 21 zuwa 51 μmol / l, amma zai iya kara zuwa 85-140 μmol / l a ƙarƙashin rinjayar jiki ko kuma a kan wasu cututtuka.
  2. Samfurin da yunwa. Yana neman gwaje-gwajen musamman (ba a sabawa) ba saboda cutar ta Gilbert. Dangane da azumi ko biyan kuɗi a cikin abinci mai rage yawan calori na kwana biyu , bilirubin a jini yana karuwa ta 50-100%. Ana auna ma'aunin bilirubin a cikin komai a ciki kafin gwaji, sannan bayan kwana biyu.
  3. Samfurin tare da phenobarbital. Yayin da ake daukar sabon abu, matakin bilirubin cikin jini ya sauko.

Yadda za a zauna tare da ciwo na Gilbert?

Haka kuma cututtukan kanta ba a dauke su da hadarin gaske ba kuma baya buƙatar takamaiman magani. Kodayake girman bilirubin a cikin jini yana cigaba a duk tsawon rayuwarsa, amma matakin da ya kamu da shi ba zai kai ga mummunar matakin ba. Sakamakon sakamakon bayyanar Gilbert yana da iyakancewa ga bayyanuwar waje da rashin jinƙai, sabili da haka, baya ga mutuwar, magani yana amfani kawai da amfani da hepatoprotectors don inganta aikin hanta. Har ila yau (a cikin lokuta masu wuya, jaundice mai tsanani) shan magungunan da ke taimakawa wajen cire sinadarai daga jiki.

Bugu da ƙari, alamun cututtuka na cutar ba su da dindindin kuma mafi yawan lokutan bazai iya ganewa ba, da karuwa tare da karfin jiki, shan barasa, yunwa, sanyi.

Abin da kawai zai iya zama haɗari shine ciwo na Gilbert - a cikin ƙananan lokuta, idan ba a daraja tsarin mulki da kuma cin abinci ba, yana taimaka wajen ci gaba da ƙonewa na biliary da cholelithiasis .

Kuma ya kamata a tuna cewa wannan cututtuka ne mai raɗaɗi, don haka idan akwai tarihin daya daga cikin iyaye, ana bada shawara don tuntube dan geneticist kafin zuwan ciki.