Hirschsprung cutar ita ce aganglion mai girma na babban hanji. Mai haƙuri ba shi da kwayoyin jikina a cikin saturan ƙwayoyi na Meissner da ƙwayar tsoka na Auerbach. Saboda rashin raguwa a cikin yankin da aka shafa kuma damuwar da aka dade a cikin wasu sassan, akwai gagarumin ƙaruwa da kuma fadadawa.
Cutar cututtuka na cutar Hirschsprung
Sakamakon farko na cututtukan Hirschsprung sune flatulence, rikice-rikice da karuwa a kewaye da ciki. Idan mai haƙuri ba ya tuntubi likita, alamun marigayi zasu fara bayyana. Wadannan sun haɗa da:
- anemia ;
- hypotrophy;
- zane-zane.
A wasu lokuta, marasa lafiya suna fama da ciwo a cikin ciki, wanda ƙarfin zai iya karuwa kamar yadda tsawon ƙarfin asibiti ya ƙaru.
Hanyoyin Hirschsprung
Ciwo na Hirschsprung yana tasowa a hanyoyi da yawa. An fara aikin farko na cutar: mai haƙuri yana da maƙarƙashiya, amma na dogon lokaci, daban-daban masu wanzuwa na shafawa suna iya kawar da shi sosai.
Bayan wannan, matakan da aka ƙaddamar da shi ya faru, yayin da yanayin rashin lafiya da rashin lafiyar marasa lafiya ya zama m. A wannan mataki na ci gaba da cutar Hirschsprung a tsofaffi, nauyin jiki yana raguwa, damuwa a cikin ciki da rashin ƙarfi na numfashi suna damuwa. A wasu lokuta, an lura da ciwon hauka mai tsanani da kuma rashin lafiya.
Matakan na gaba na cutar ya raguwa. Ba a tallafa wa marasa lafiya ta hanyar wankewar enemas da sauran laxatives. Har yanzu tana jin damuwa a cikin ƙananan ciki, kuma haɗarin hanzarin hanzari ya karu da sauri.
Sanin asalin cutar Hirschsprung
Idan ana tuhuma da cutar Hirschsprung, ana gudanar da jarrabawar gwanin farko. A gaban cutar, an samo ampoule mara kyau na dubun a cikin mai haƙuri. An ƙara sauti na sphincter. A wannan yanayin, wajibi ne a dauki radiyo na binciken dukkanin sassan ɓangaren na ciki. Tare da cututtukan Hirschsprung, an rufe ɗakunan bugun jini da kuma fadi, wasu lokuta ana gano nauyin ruwa.
Har ila yau mai haƙuri ya buƙaci shawo kan sigmoidoscopy, irrigography, colonoscopy da diagnostics histochemical.
Jiyya na cutar Hirschsprung
Hanyar da za a bi da cutar Hirschsprung ne tiyata. Babban manufofin aiki shine:
- da ruwa da dukkanin sassan;
- kawar da yankin aganglionic;
- adana ɓangare na babban hanji wanda ke aiki.
Ga yara, an gudanar da ayyukan Swanson, Duhamel da Soave. Mazan da suka yi a cikin nau'i na al'ada an hana su sabani saboda fasalin fasalin mutum da kuma sclerosis mai tsanani a cikin ƙwayoyin ƙwayoyin jijiyoyin muscular ko ƙananan hanyoyi na hanji. Mafi sau da yawa, tare da cutar Hirschsprung, Duhamel yana aiki ne, wanda aka cire yankin da ake yi da aganglionary tare da ƙirƙirar kututture na ɗayan. A mafi yawancin lokuta, yana yiwuwa ya hana lalacewa ga sphincter na anus kuma ya haifar da anastomosis na al'ada.
Kafin yin aiki, mai haƙuri yana bukatar
Sanarwar gaba daya game da cutar Hirschsprung bayan yin aiki yana da kyau. Amma a wasu lokuta, ana iya buƙatar sake tiyata. Kusan kullun ainihin irin wannan aiki an rage shi zuwa sake sake fasalin anastomosis kuma ana gudanar da ita ta hanyar peritoneal ko perineal access.