Purpura Thrombocytopenic - menene haɗarin cutar?

Duk nau'in cututtuka na jini (hemorrhagic) abu ne na al'ada a maganin zamani. Kimanin kashi 50 cikin dari na ƙwayoyin cuta ne mai tsarki na thrombocytopenic, wasu dalilai suna da yawa kuma basuyi kama juna. Wannan cuta tana rinjayar jiki a kowane zamani.

Purpura thrombocytopenic - haddasawa

Binciken Verlhof ko kuma mai tsabta na thrombocytopenic, wadanda ba a san su ba har sai yanzu - wani abu wanda wani masanin kimiyyar Jamus ya gano a baya a 1735. A cikin mutane an kira shi "cututtukan cututtuka" saboda a cikin irin wannan marasa lafiya a jikin jiki a nan kuma a can yana bayyana lalacewa daban-daban.

Cututtuka, a mafi yawan lokuta, yana faruwa a yara daga haihuwa zuwa ƙuruciya, sa'an nan kuma zai iya ɓacewa gaba ɗaya ba tare da maganin warkewa ba. A cikin yara a ƙarƙashin shekara biyu, lokuta masu tsarki ne ake rubutawa a cikin yara. A lokacin balagagge, an gano wannan asali ga marasa lafiya 1-13 daga mutane 100,000, tare da mafi yawan lokuta masu zama mace.

Forms na thrombocytopenic purpura

Kwayar jini kamar cututtukan thrombocytopenic (cututtukan Verlhof) yana faruwa a lokacin da jini - plalets, suna shafe su da tsarin kansu kuma sun mutu ba tare da gangan ba. Lokacin rayuwarsu a maimakon kwanaki 7-10, yana da sa'o'i da yawa. Don samar da masu tsauraran kai tsaye, hakin yana da alhaki. Kwayar cuta tana da siffofin da yawa wanda ya dogara ne akan cutar, amma ya bambanta a cikin bayyanar cututtuka:

Hanyoyin tsarkakewa na idon na thrombocytopenic, duk da mawuyacin haddasawa, sun kasu zuwa:

Tsarin mai amfani na thimbocytopenic na Autoimmune

A wasu lokuta, jiki yana fara aiki da kansa. Wannan nau'i ne na irin wannan cuta. An kawar da platelets ta hanyar rigakafi, wanda ke gane su a matsayin ƙwayoyin waje. Irin wannan cututtukan wani lokaci yakan faru a kan tushen wani tsari na jiki a jiki. Tsuntsauran thrombocytopenic masu tsauri na al'ada yana haifar da lalacewar kayan ado na kanta a ƙarƙashin rinjayar abubuwa da dama. Wani lokaci wannan nau'i ne na kwayoyin halitta, ko da yake a mafi yawan lokuta dalilai wadanda cutar ta faru sune kamar haka:

Purroimmune thrombocytopenic purpura

A lokacin haihuwa, cutar kwayar cutar kwayoyin cutar kwayoyin cuta (thrombocytopenic) tana da yawa sau da yawa fiye da manya. Labari mai dadi shi ne cewa samin yara don dawowa yana da kyau. Dalilin cutar shine:

Purpura Thrombocytopenic - bayyanar cututtuka

Kwayar cutar Verlhof, wanda alamunta ya kasance mai basira, ya bambanta daga lokacin bayyanar lalata. Wato, a farkon, bruises ko, kamar yadda aka kira su da likitoci - petechiae, an bayyana su a hankali, sannu-sannu rage ƙananan launi kuma sun zama cikin cyanotic, kore ya, da hankali juya launin rawaya. A wani lokaci a lokaci, kowane nau'i na wulakanci zai iya zama a jiki, wanda shine hoto mai ban mamaki, amma ba su da wata azaba, ba kamar raunin da ya faru ba a cikin mutum mai lafiya.

An yi amfani da Bruises a kan ƙananan ƙafa, sau da yawa a jiki, kuma yana da wuya a fuskanta, amma mucous banda. Tsabtace Thrombocytopenic yana da alamun kamuwa da juna a cikin mutane daban-daban. Za su iya tashi a sakamakon microtrauma, kuma ba tare da wani dalili ba. Mahimmanci, labarun yana faruwa a daren. A wannan yanayin, mai yin haƙuri ba zai fuskanci ciwo ba, sai dai yanayin jinji, lokacin da mai hankali ya bukaci asibiti. Bambanta:

Sanin asali na purin thrombocytopenic

Binciken maganin Verlhof, ƙididdiga wadda ba ta ƙare tare da ganewar bayyanar cututtuka ba, yana dogara ne akan sakamakon bincike na binciken marasa lafiya da jarrabawa. Doctors yi wani kayan aiki yayin da thrombocytopenic purpura bayyana kanta a karon farko. Bayan da aka gano cututtukan da suka dace da su kuma ana gudanar da nau'o'in karatu daga jini don nazarin, kafin a gudanar da gwajin jini. Wadannan sun haɗa da:

  1. Gwajin gwajin , lokacin da aka sanya macijin don maganin matsa lamba a minti 10. Idan a karshen wannan lokacin dots na jini da aka kafa a karkashin kullun, gwajin ya tabbata. An yi shi a cikin yara daga shekara uku.
  2. An gwada gwajin lokacin da ake amfani da baza'in likita a hannun, wanda bayan dan lokaci ya ba da kurma - wannan hanya ya dace da marasa lafiya marasa lafiya.

Tsabtace Thrombocytopenic, ya ƙunshi jerin gwaje-gwaje da za su nuna hoto mai dogara game da jinin marasa lafiya. Wadannan sun haɗa da gwajin jini don:

Bugu da ƙari, a cikin lokuta mai tsanani ko rashin daidaituwa da sauran nau'o'in ganewar asalin mai tsarki na thrombocytopenic, anyi amfani da maniyyi na kasusuwan - trepanabiopsy. Tare da taimakon kayan aiki na musamman, an yi ƙananan ƙuƙwalwa a cikin yankin lumbar don ɗaukar ƙananan kasusuwa na kayan ƙashi, periosteum da kuma ruwan sanyi don bincike.

Purpura Thrombocytopenic - magani

Cututtuka na jini yana buƙatar halayya mai tsanani, saboda lafiyar mai haƙuri a kowane zamani ya dogara da girman wannan. Jiyya na thrombocytopenic purpura ne da za'ayi biyu a asibiti (a lokacin wani lokaci na exacerbation) da kuma a gida. Dole ne a ba marasa lafiya da iyakar iyakoki da kwanciyar gado don rage yawan lokutan traumatic. Dangane da wannan batu, ana amfani da hanyoyin al'adun gargajiya tare da maganin mutane. Yana da matukar muhimmanci a biye da wani abinci.

Ta yaya warkar ne cutar Verlhof?

Ya danganta ne a kan shekarun da kuma a wane mataki ne aka gano cutar Verlhof, za a yi tambaya game da lafiyarta. A lokacin haihuwa, halayen yana tabbatacce, idan an gano jaririn da wuri kuma ya samu nasara a cikin watanni shida. Bayan wannan lokaci, ganewar asali ya zama mai ci gaba, kuma yana da mahimmanci kamar thrombocytopenia.

Matasa ba su da wadata - wannan yanayin zai iya biye da su a cikin rayuwarsu tare da jinkirta gafara da yunkuri. A wasu lokuta, mai tsabta na thrombocytopenic na yau da kullum zai iya warkewa lokacin da aka cire rami, ko da yake wannan ba ya tabbatar da 100%. Wannan kwayar ta rushe platelets kuma ita ce makiyi na jiki. Ana amfani da wannan hanya azaman gardama na ƙarshe, lokacin da sauran nau'in magani basu da amfani. Yi aiki a matsayin hanyar cavitary, tare da taimakon wani laparoscopy.

Purpura Thrombocytopenic - kwayoyi

Manufar tsarin kula da cutar Verlhof ita ce kula da matakin platelets a cikin jini a matakin da ake bukata. An shafe mummunan thrombocytopenic mai tsauri da cuta, a cikin mafi yawancin lokuta da suka samu nasara, wanda ya ba da damar yin gyare-gyaren barga na shekaru masu yawa. Idan ba magani ko aiki ya taimaka ba, an canza makirci don shan magunguna zuwa sabon abu. Don yin wannan, yi amfani da:

  1. Prednisolone (Methylprednisolone) wani maganin miyagun ƙwayoyi ne na steroid, don rage aikin rigakafi. An yi amfani dashi a farkon matakai na magani, kafin a cire kauyen.
  2. Ana amfani da Interferon a2 don kawar da kwayoyin cutar kansa, lokacin da kwayoyi masu steroid basu da ƙarfi.
  3. Ana amfani da immunoglobulin G kafin a tiyata don ƙara yawan platelets.
  4. Immunosuppressants (Cyclophosphamide, Vincristine da Azathioprine) ana amfani dashi lokacin da marasa lafiya suka gane wani magani. Akwai dakatar da kwayoyin cuta a cikin jini, wanda hakan zai haifar da karuwa a yawan adadi.
  5. Magungunan magani Danazol, mai da hankali ga glandan gwal tare da dogon liyafar yana da tasirin tasirin jini.

Purpura Thrombocytopenic - magani tare da magunguna

Mutuwar thrombocytopenic m shine cutar jini, sabili da haka ana shirye-shiryen magani na kayan lambu (decoctions) tare da magungunan hemostatic don maganin sa:

Cin abinci tare da mai cin hanci na thrombocytopenic

Babu abinci na musamman ga rashin lafiya na Verlhof. Yana da muhimmanci cewa ana amfani da jita-jita a cikin ɗan ƙaramin sanyi ko sanyi. Kayan kayan lambu tare da tsirrai na thrombocytopenic, kamar 'ya'yan itatuwa suna da amfani amma basu kamata su haddasa allergies ba. Jerin samfurorin samfurorin sun hada da:

Dole ne ku ware daga abinci:

Purpura Thrombocytopenic - rikitarwa

Kwayar cutar Verlhof, wanda matsalolinsa suna da hatsarin gaske, dole ne a kula da lafiyar likita. Abubuwa sun hada da:

Purpura Thrombocytopenic - rigakafi

Lokacin da aka gano wani mai ciki da "thrombocytopenic purpura," wannan yana nufin cewa don lafiyar mutum daya dole ne ya bar yawancin halaye, da cutarwa da kuma talakawa, sauye-sauye na rayuwa. Tsarin hanzari na nufin ci gaba da karɓar platelets da hemoglobin saboda cin abinci masu cin abinci, da kuma cire irin wadannan abubuwa masu fasikanci: