Werlhof ta cutar

Werlhof ta cutar - thrombocytopenic purpura - wata cuta bayyanar a cikin nau'i na hemorrhagic jijjiga a kan tushen da ƙara yawan (gluing) na platelets. Kamfanin microthrombi da aka ƙera ya zubar da ƙananan ƙararrawa. Bugu da ƙari, akwai ƙwayar jini da kuma karuwar yawan adadin tallan.

Sanadin cututtukan Werlhof

A halin yanzu, ba a san ainihin asalin thrombocytopenic purpura ba. Yi amfani da siffofin na farko da na sakandare na cutar Verlhof. Fassara na asali sune asali ne a cikin yanayin ko bayyanar sakamakon sakamakon cutar. Misalai na biyu sunyi alamun wasu cututtuka.

Cutar cututtuka na cutar ta Verlhof

Kwayar ta fara farawa, saboda babu wani dalili, wani lokaci akan bango na cututtuka na intestinal ko ARI. A cikin mai haƙuri a farkon mataki, wadannan halaye bayyanar cututtuka ne m:

Alamar babbar ita ce cututtuka da ƙananan cututtuka, wanda ya bayyana sunan na biyu na cutar - purin thrombocytopenic.

Bayan ɗan gajeren lokaci, ciwo mai kwakwalwa yana nuna kansa musamman a cikin hanyar:

Harkokin ilmantarwa suna tare da cututtukan neurological, kamar:

A cikin lokuta masu tsanani, yana yiwuwa a bunkasa ƙaƙa.

Gudun ciki a karkashin fata ya zama mai yawa kuma ya kasance a babban yanki. Dangane da takardar sayan magani, lafazin suna da launi daga launin ja-launin ruwan kasa zuwa launin rawaya (kamar tsohuwar ƙura).

Sakamakon ganewar cutar Verlhof ya fara ne tare da jarrabawa da kuma motsi. Cibiyar bincike ta haɗa da gwaje-gwaje masu zuwa:

  1. Babban bincike na jini (OAK). An ƙaddamar da cutar ta rage matakin erythrocytes da hemoglobin, rage yawan platelets da gano kwayoyin cutar antipletlet.
  2. Sternary puncture - shan kasusuwa kashi don jarrabawa ta hanyar wani sternum fashewa. A cikin nazarin kwayoyin halitta, an samu karuwa a yawan megakaryocytes, adadi kaɗan na platelets, yayin da babu sauran canje-canje a cikin kasusuwan kasusuwa, alal misali, wadanda suke da alamun tsarin ciwon tumo.
  3. Trepanobiopsy - nazarin kasusuwan kasusuwa tare da periosteum da kasusuwa (daga yankin pelvic), tare da taimakon na'urar kiwon lafiya ta trephine. Tare da cutar na Verlhof, rabo daga ƙwayar nama da hematopoietic ya dace da al'ada.

Jiyya na cutar Verlhof

Matakan kiwon lafiya sun dogara ne akan tafarkin cutar. Ana gudanar da jiyya ta hanyar daya daga cikin wadannan hanyoyin:

  1. Yin amfani da corticosteroids don dalilan kama da ciwon halayen jini da kuma kara yawan platelets cikin jini. Prednisalon an tsara shi a wata nau'i na 1 MG da 1 kilogiram na nauyin haƙuri a kowace rana. Idan akwai wani mummunar cuta na cutar, za'a ninka kashi biyu.
  2. Idan ba a samu sakamako mai kyau ba, ana bada shawara ga mai yin haƙuri don cire ƙwan zuma . A cewar kididdiga na likita, a cikin kashi 80 cikin dari na marasa lafiya bayan an yi amfani da maganin rigakafi sosai.
  3. A wasu lokuta da yawa, bayan da aka yi amfani da kwayar cutar, jini yana wucewa, kuma cutar ta kasance, an riga an umarci immunosuppressants (Azathioprine, Vincristine) da glucocosteroids.

Don cire bayyanar cututtuka na rashin ciwon halayen jini, ana amfani da magungunan haemostatic: