Myasthenia gravis - bayyanar cututtuka

Myasthenia gravis yana daya daga cikin cututtuka masu banƙyama, wanda yawancin ya shafi mutane a lokacin ƙuruciyarsu. Hakanan daga harshen Helenanci an fassara wannan taken a matsayin "ƙwayar tsoka", wanda ke taƙaice bayanin ainihin alamar. A al'ada, bamu magana game da raunin tsohuwar tsoka ba, wanda mutane ke shafar bayan motsa jiki. A nan tambaya ita ce mafi tsanani - damuwa ta ilimin halitta na musculature mai tsanani, yafi da kai da wuyansa.

Ayyuka da Facts

A karo na farko cutar cututtuka na myasthenia aka bayyana a cikin tarihin karni na 17, kuma a karni na 19 ya samo sunan sunan. An yi amfani da maganin miyagun ƙwayoyi mai mahimmanci a tsakiyar karni na 20, tare da inganta yawan kwayoyi.

An kirkiro Myasthenia a matsayin cututtuka na asali, wanda shine, inda jikin mutum ya fara samuwa daga kwayoyin cutar da aka tsara akan jikinsa mai lafiya da kyallen takarda da kuma ci gaba da halayen mai kumburi.

An san cewa sau da yawa tare da alamun myasthenia gravis akwai mata, kuma cutar ta fara bayyana kanta a lokacin yaro, daga 20 zuwa 40 shekaru. Har ila yau, akwai lokuttan da ake kira myasthenia gravis, wanda shine mai yiwuwa a raba shi. Haka kuma cutar ba ta da wuya, kimanin kashi 0.01 cikin 100 na yawan jama'a, amma likitocin suna kallo ne akan yawan lokuta.

Abubuwan da aka sani da kuma abubuwan da suka faru na ƙwarewar myasthenia gravis

Hanyar aikin ci gaba na myasthenia yana dogara ne akan cin zarafi ko kuma rufe cikakken aikin aikin neuromuscular. Wannan yana faruwa a ƙarƙashin rinjayar kwayoyin cuta, wanda ake samar da shi ta hanyar rigakafi (autoimmune reaction). Sau da yawa, muhimmiyar rawa a cikin wannan tsari tana taka leda na thymus - kwayar halittar kwayoyin halitta, wanda ake kiyaye ciwon ciwon daji. Tare da irin wannan cuta, likitoci suna kira na farko yana haifar da maye gurbin sunadaran sunadarai, wanda ke shiga cikin haɗin neuromuscular.

Doctors sun gano wasu abubuwa masu tayar da hankali da suke kara cutar da cutar:

Bayanin na asibiti

Myasthenia gravis yana nuna kansa a wasu cututtuka daban-daban, wanda aka haɗuwa zuwa wasu siffofin:

  1. Eye. Har ila yau, sau da yawa shine mataki na farko na cutar. Ana bayyana shi ta hanyar ragewa (ptosis) na fatar ido (ko daya), strabismus, da hangen nesa biyu a idanu, wanda za'a iya kiyaye duka a cikin jiragen da ke tsaye da kuma kwance. Kwayar cututtukan ƙwayar cuta yawanci ne - watau, sun canza a ko'ina cikin yini - suna da rauni a safiya ko ba su nan ba, kuma mafi tsanani ne da maraice.
  2. Bulbarnaya. A nan, tsokoki na fuska da larynx na farko sun shafi, sakamakon abin da mai haƙuri ke da murya na hanci, fuska fuska fuska fuska, kuma abubuwan da suka faru na dysarthritic sun bayyana. Har ila yau, aikin haɗiye da gyare-gyare na iya zama damuwa, daidai a tsakiyar abincin. Yawancin lokaci, bayan hutawa, ana mayar da ayyukan.
  3. Rashin rauni a cikin tsokoki na ƙwayoyin hannu da wuya. Marasa lafiya ba zai iya ɗaukar kawunansu a hankali, gawar ya karya, yana da wuya a ɗaga hannuwan ko ma tashi daga kujera. A wannan yanayin, koda karamin karamin jiki yana kara yawan bayyanar cutar.

Myasthenia gravis zai iya bayyana kanta a cikin gida da kuma na kowa, wanda aka la'akari da ya fi tsanani, tun da zai iya ɓata ayyukan da na numfashi. Kwayar yana da yanayin ci gaba, tare da bayyanar da jihohi da dama, ba tare da izinin hutawa ba, har ma da crises, wanda zai iya haifar da mutuwa. Sabili da haka, idan kana da wasu alamomi, kana buƙatar ganin likita.